Access the full text.
Sign up today, get DeepDyve free for 14 days.
Marie Robert, A. Hot (2022)
Atrophic PapulosisDermatology, 239
P. Song, Shufeng Li, Matthew Lewis, D. Fiorentino, L. Chung (2023)
Clinical Associations of Degos-Like Lesions in Patients With Systemic Sclerosis.JAMA dermatology
S. Giacalone, C. Moltrasio, G. Nazzaro (2019)
Degos-Like Cutaneous Findings in an Adult Woman With NXP-2-Associated Dermatomyositis.JAMA dermatology
( Robert M , Hot A . Atrophic papulosis. Dermatology 2023;239:177–87.36353773)
Robert M , Hot A . Atrophic papulosis. Dermatology 2023;239:177–87.36353773Robert M , Hot A . Atrophic papulosis. Dermatology 2023;239:177–87.36353773, Robert M , Hot A . Atrophic papulosis. Dermatology 2023;239:177–87.36353773
( Song P , Li S , Lewis MA , et al. Clinical associations of degos‐like lesions in patients with systemic sclerosis. JAMA Dermatol 2023;159:308–13.36753129)
Song P , Li S , Lewis MA , et al. Clinical associations of degos‐like lesions in patients with systemic sclerosis. JAMA Dermatol 2023;159:308–13.36753129Song P , Li S , Lewis MA , et al. Clinical associations of degos‐like lesions in patients with systemic sclerosis. JAMA Dermatol 2023;159:308–13.36753129, Song P , Li S , Lewis MA , et al. Clinical associations of degos‐like lesions in patients with systemic sclerosis. JAMA Dermatol 2023;159:308–13.36753129
( Giacalone S , Moltrasio C , Nazzaro G . Degos‐like cutaneous findings in an adult woman with NXP‐2‐associated dermatomyositis. JAMA Dermatol 2020;156:218–20.31876929)
Giacalone S , Moltrasio C , Nazzaro G . Degos‐like cutaneous findings in an adult woman with NXP‐2‐associated dermatomyositis. JAMA Dermatol 2020;156:218–20.31876929Giacalone S , Moltrasio C , Nazzaro G . Degos‐like cutaneous findings in an adult woman with NXP‐2‐associated dermatomyositis. JAMA Dermatol 2020;156:218–20.31876929, Giacalone S , Moltrasio C , Nazzaro G . Degos‐like cutaneous findings in an adult woman with NXP‐2‐associated dermatomyositis. JAMA Dermatol 2020;156:218–20.31876929
The patient, a 32‐year‐old woman with a history of NXP‐2 dermatomyositis, presented to the combined rheumatology‐dermatology clinic for evaluation of a 6‐month history of painful, enlarging, and draining ulcers on her left thigh. Prior treatment with antibiotics had not resulted in improvement. She also has myositis (based on elevated creatine kinase and aldolase levels and muscle inflammation on magnetic resonance imaging), joint pain, dysphagia, and gastroesophageal reflux disease. Skin examination revealed a 2 × 2 cm ulcer with an overlying hemorrhagic crust and minimal purulence. In the surrounding skin (porcelain‐white) atrophic macules with an erythematous rim on a background of reticulated erythematous patches were noted (A). The patient did not have other classic cutaneous findings of dermatomyositis. A punch biopsy of a macule demonstrated lymphocytic vasculitis (B, part 1) with superficial dermal hyalinization (B, part 2), which is compatible with Degos disease. Two years after her diagnosis, ulcerative lesions have abated, and muscle strength significantly improved. The patient is being treated with intravenous immunoglobulins, azathioprine, steroids, aspirin, and topical tacrolimus. She also continues to work with physical therapy. Degos disease is a rare vascular occlusive disorder of unknown etiology. It can present in a benign or malignant form (1). The benign
ACR Open Rheumatology – Wiley
Published: Sep 1, 2023
Read and print from thousands of top scholarly journals.
Already have an account? Log in
Bookmark this article. You can see your Bookmarks on your DeepDyve Library.
To save an article, log in first, or sign up for a DeepDyve account if you don’t already have one.
Copy and paste the desired citation format or use the link below to download a file formatted for EndNote
Access the full text.
Sign up today, get DeepDyve free for 14 days.
All DeepDyve websites use cookies to improve your online experience. They were placed on your computer when you launched this website. You can change your cookie settings through your browser.